Psychiatric comorbidity in Prader-Willi syndrome. A case of atypical bipolar disorder

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Published

2016-03-17

How to Cite

Girela Serrano, B., Calvo Rivera, M. P., & Herreros, Óscar. (2016). Psychiatric comorbidity in Prader-Willi syndrome. A case of atypical bipolar disorder. Revista De Psiquiatría Infanto-Juvenil, 33(1), 38–42. https://doi.org/10.31766/revpsij.v33n1a5

Issue

Vol. 33 No. 1 (2016)

Section

Case reports
Crossref
Scopus
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Europe PMC

Authors

  • Braulio Girela Serrano
  • María Pilar Calvo Rivera
  • Óscar Herreros

DOI:

https://doi.org/10.31766/revpsij.v33n1a5

Keywords:

Prader-Willi syndrome, Bipolar Disorder, Cycloid Psychosis, Lithium

Abstract

Prader-Willi syndrome (PWS) is a known neurodevelopmental genetic disorder secondary to lack of expression of the genes of the 15q11-q13 region allele of paternal origin, with an estimated prevalence of 1:25000 births. It is characterized by the presence of dysmorphia, short stature, hypogonadism, overweight, and a behavioral phenotype with learning disabilities, mental retardation, rituals, stereotypies and compulsive behaviors, skin-picking, frequent tantrums, irritability, and hyperphagia. The SPW is also associated with an increased risk of psychiatric symptoms, most notably by its severity psychoses and affective disorders.


It is presented the case of a 12-years-old male diagnosed with SPW in which suddenly appears an atypical psychotic episode, discussing both its diagnosis and therapeutic intervention in the light of the published scientific literature.

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Author Biographies

Braulio Girela Serrano

MIR de Psiquiatría, Hospital Santa Ana, Motril, Granada

María Pilar Calvo Rivera

MIR de Psiquiatría, Complejo Hospitalario Universitario de Granada

Óscar Herreros

Psiquiatra Facultativo Especialista de Área, USMIJ, Complejo Hospitalario Universitario de Granada

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